segunda-feira, 2 de novembro de 2009

ESCLEROSE TUBEROSA...



Shagreen patch of Tuberous SclerosisKetan Kulkarni Department of Pediatrics, PGIMER, Chandigarh, India Address for correspondence: Dr Ketan P Kulkarni, APC, PGIMER, Chandigarh, India Email: ketanpkulkarni@gmail.com A 10 year old female child presented with polymorphic seizures and skin patch. She also had adenoma sebaceum. Neuroimaging demonstrated multiple subependymal nodules with candle dip appearance. What Is the diagnosis_? What is the skin lesion_?

The diagnosis was clearly tuberous sclerosis. Skin lesion is Shagreen patch. E-published: December 2008, Vol 5 Issue 12 Art # 51

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